Abstract: To investigate clinical approach of bone and soft tissue reconstruction and fixed implant restoration for dysplasia patient. Jaw reconstruction was done by iliac graft with digital guide and implants were placed under surgical guide. Free gingiva graft and second stage surgery was applied after implant osseointegration. Function and esthetic outcome was verified through fixed temporary restoration. Full arch screw retained fixed prosthesis was delivered for final restoration. Bone volume was good enough for implant placement. Implant ossteointegration was successful with enough keratinized tissue around implant after free gingiva graft. Patient was satisfied with the esthetic and masticatory function. The result was stable at 24 months follow-up. Fixed implant restoration for ectodermal dysplasia patient after hard and soft tissue augmentation was an effective therapy approach. Short-term result was stable.